Prosthodontic Rehabilitation of a patient with Hutchinson Gilford Progeria Syndrome: a rare case report

Abstract

Progeria is a rare genetic disease where symptoms resembling aspects of aging are manifested at an early age. Characteristic clinical findings of Progeria include abnormalities of the skin and hair in conjunction with characteristic facial features and skeletal abnormalities. The findings that are nearly interested in dentistry are delayed dentition, anodontia, hypodontia, or crowding of teeth. Psychological trauma is common in such patients because of the societal alienation they often face; hence, the successful completion of any treatment modality in such patients is affected by how well the Prosthodontist handles their psychological condition. This report follows the Prosthetic rehabilitation of a patient suffering from Hutchinson Gilford progeria syndrome with congenital anodontia , keeping special attention  on psychological behaviour. Rehabilitation of such a compromised complete denture patient  in a conventional manner possess many challenges. To overcome these challenges certain modifications in treatment procedure and materials used were made to fulfil the patient’s functional, esthetic and psychological demands.